Repair of all the components of the syndrome of aortic regurgitation and VSD

Evdokia Petropoulou1, Stergios Theodoropoulos1 and Magdi H. Yacoub2,*

1IASO General Hospital, Athens, Greece
2Imperial College of Science, Technology and Medicine, National Heart and Lung Institute at Heart Science Centre, Harefield, Middlesex UB9 6JH, UK

* Corresponding author. Tel: +44 1895 453893; fax: +44 1895 828902. E-mail address: m.yacoub{at}imperial.ac.uk

There is still no agreement about the need for, timing, and type of repair of the Syndrome of VSD and AR (syndrome of Laubry and Pezzi). The syndrome is commonly thought of as due to a simple prolapse of the aortic leaflet into a ‘high’ VSD. We believe that the syndrome is caused by congenital discontinuity of the media of the aortic sinus from the crest of the interventricular septum. This results in aneurismal dilatation and bulging of the right coronary sinus into the RVOT, VSD, and prolapse of the aortic cusp. Images in this report illustrate all the anatomical components both before and after repair using a simple technique described previously by us.

Panel A. The discontinuity between the aortic media and the crest of the septum, the longitudinal dilatation of the sinus of Valsava, the prolapse of the cusp, and lack of coaptation of the aortic cusps. This was associated with moderate aortic regurgitation with a jet directed towards the anterior mitral leaflet (Panel C). During systole, the VSD shunt is apparent (Panel E), while in diastole the dilated sinus and prolapsing cusp obstruct the VSD (Panel C). Following simple transaortic repair, re-attachment of the crest of the septum to the aortic media results in closure of the VSD, correction of the dilated sinus, elevation of the aortic cusp with increased coaptation (Panel B), and marked improvement in AR, which become ‘trivial’ (Panel D). There were no shunts detected during systole (Panel F) or diastole (Panel D).


{ehi52401}





This Article
Full Text (PDF)
All Versions of this Article:
26/24/2629    most recent
ehi524v1
Alert me when this article is cited
Alert me if a correction is posted
Services
Email this article to a friend
Similar articles in this journal
Similar articles in PubMed
Alert me to new issues of the journal
Add to My Personal Archive
Download to citation manager
Request Permissions
Google Scholar
Articles by Petropoulou, E.
Articles by Yacoub, M. H.
PubMed
PubMed Citation
Articles by Petropoulou, E.
Articles by Yacoub, M. H.